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Darier's Disease

What is this rash? My father also has it.
Darier disease is a stubborn rash which usually runs in families. The rash often starts when one is a teenager or older. It most commonly affects the chest, neck, back, ears, forehead, and groin, but may involve other body areas. At times, the rash will cause a bad odor. This disease can also cause the fingernails to be fragile at the tips causing V-shaped notches at the end of the nails as pictured below.

What causes it?
The cause is thought to be due to a defective gene. The gene that causes Darier disease is often inherited from one's parents. Darier disease is not contagious; that is, it does not spread from person to person. The rash is often worse in the summer, due to the heat and humidity, and is aggravated by sunlight.

How do I treat it?
Cleansing the skin with a mild antibacterial soap such as Lever 2000 or Dial antibacterial sometimes helps control the odor. Dr. Guccione may give you a prescription for a gel or lotion to use on your skin.

There is no medical cure for Darier disease. A strong drug called Accutane sometimes helps this condition. Dr. Guccione will discuss the possible use of this medication with you.